Laugier–hunziker Syndrome
Laugier–hunziker syndrome. There is no underlying systemic abnormality or malignant predisposition. Herein we reported a 45-year-old female case with LHS. 2 Since its first description by Laugier and Hunziker in 1970 10 more than 100 cases have been described world wide.
Although it is unknown what causes this rare disorder it seems to affect more adult women than men. WHAT IS LAUGIER-HUNZIKER SYNDROME. It is associated with lenticular or linear hyperpigmented macules that can be isolated or confluent and that can present in various mucocutaneous tissues.
Laugier-Hunziker syndrome LHS was initially described in 1970 as acquired benign hyperpigmented macules of the lips and buccal mucosa frequently. It usually appears on the oral mucosa which covers the major portion of the mouth except that of teeth. Laugier-Hunziker syndrome also known as Laugier-Gerbig-Hunziker syndrome or Laugier-Hunziker-Baran syndrome or idiopathic lenticular mucocutaneous pigmentation is a hereditary pigmentary disorder characterized by a unique expression.
This condition is known to be an entirely benign disease with no systemic manifestations. GARD Answers GARD Answers Listen. Questions sent to GARD may be posted here if the information could be helpful to others.
LHS also known as idiopathic lenticular mucocutaneous pigmentation is a benign pigmentary disorder without systemic symptoms. We remove all identifying information when posting a. Physical Examination Oral pigmentation 6 10 11 12 is most commonly present on the buccal mucosa and the lips usually the lower lip but it can also occur on the gingiva the tongue the.
Although a limited number of familial cases have been reported no putative genetic defects have been identified and this is generally thought to be an acquired condition. Laugier-Hunziker syndrome is a harmless rare sporadic disorder that is characterised by flat brown marks on the lips and inside the mouth and frequently brown stripes on the nails. Laugier-Hunziker syndrome LHS is an acquired benign pigmentary skin condition involving oral cavity including lower lip in the form of brown black macules 1-5 mm in size frequently associated with longitudinal melanonychia.
Laugier-Hunziker syndrome is a sporadic condition characterised by essential acquired and benign melanotic pigmentation of the oral cavity and lips which is often associated with spotted macular pigmentation of the fingertips and longitudinal melanonychia. The spots are less than 5mm in diameter and are benign.
The condition has been described most often in Europe with a predilection for white females.
Laugier-Hunziker syndrome LHS was initially described in 1970 as acquired benign hyperpigmented macules of the lips and buccal mucosa frequently. We want to hear from you. Laugier-Hunziker syndrome LHS is a rare benign condition of macular hyperpigmentation of mucocutaneous surfaces and nails. Fewer than 200 cases have been reported in the literature. This condition is known to be an entirely benign disease with no systemic manifestations. Physical Examination Oral pigmentation 6 10 11 12 is most commonly present on the buccal mucosa and the lips usually the lower lip but it can also occur on the gingiva the tongue the. Laugier-Hunziker syndrome is a rare idiopathic acquired hyperpigmentation of oral mucosa and lips which is often associated with longitudinal melanonychia. It is associated with lenticular or linear hyperpigmented macules that can be isolated or confluent and that can present in various mucocutaneous tissues. Do you have updated information on this disease.
The spots are less than 5mm in diameter and are benign. GARD Answers GARD Answers Listen. The condition has been described most often in Europe with a predilection for white females. It is associated with lenticular or linear hyperpigmented macules that can be isolated or confluent and that can present in various mucocutaneous tissues. It usually appears on the oral mucosa which covers the major portion of the mouth except that of teeth. 2 Since its first description by Laugier and Hunziker in 1970 10 more than 100 cases have been described world wide. This condition is known to be an entirely benign disease with no systemic manifestations.
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